Anesthetic Strategy for a Femur Fracture Surgery in a Patient with Hemophilia B (Factor IX Deficiency): A Case Report
نویسنده
چکیده
Hemophilia is a hemorrhagic trend affects mostly males (X-related recessive disease). In 85% of cases it is caused by factor VIII deficiency, being called hemophilia A or classic hemophilia. In approximately 15% of cases there is factor IX deficiency (hemophilia B).[1-3] Hemophilia B is characterized into severe (<1%), moderate (1%–5%), or mild (5%–40%) phenotypes in light of the plasma component IX action of influenced people.[4] A variety of underlying mutations have been identified and linked with different levels of clinical severity.[4,5] The serious phenotype is portrayed by unconstrained and repetitive draining scenes into joints and muscles, with hemarthroses being the dominating reason for long haul disability.[5] The moderate phenotype is described by incidental unconstrained drains and delayed seeping with minor injury or surgery. At last, patients with the gentle phenotype once in a while exhibit unconstrained draining yet may have critical seeping with significant injury or surgery. Forceful component substitution is required fundamentally for patients with moderate and serious hemophilia B phenotypes.[1,4] Hemophilia ought not to be a contraindication for an invasive procedure; be that as it may, various conditions are required to give fruitful surgery and an uncomplicated and safe postoperative course.[6] In any capacity, when these patients are submitted to surgical procedures, it merits uncommon consideration and a multidisciplinary group of wellbeing experts educated about the sickness, including qualified hematologist, surgeon and anesthesiologist.[3,7,8] The objective of this report was to describe the case of a patient with Hemophilia B underwent a femur fracture surgery.
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